Hirschsprung’s Disease, A Simple Guide To The Condition, Diagnosis, Treatment And Related Conditions

By Kenneth Kee

Hirschsprung’s disease is a congenital disorder causing blockage of the large intestine.
It happens due to poor muscle movement in the bowel.
The underlying pathology is the absence of parasympathetic ganglion cells in the myenteric and sub-mucosal plexus of the rectum, and sometimes also in the colon.
Normally 24h) is very important because:
50% of all Hirschsprung’s patients do not pass meconium within 36h
50% of all children with delayed passage of meconium have Hirschsprung’s disease
Rectal examination often reveals the narrowing of the rectosigmoid colon.
When the finger is withdrawn, there may be evacuation of a watery stool.
Symptoms in older children:
1. Constipation that slowly becomes worse
2. Fecal impaction
3. Malnutrition
4. Slow growth
5. Swollen belly
Milder cases may not be diagnosed until the baby is older.
During a physical exam, the doctor may be able to feel loops of bowel in the swollen abdomen.
A rectal exam may indicate tight muscle tone in the rectal muscles.
Tests used to help diagnose Hirschsprung's disease may be:
1. Abdominal x-ray
2. Anal manometry (a balloon is inflated in the rectum to measure pressure in the area)
3. Barium enema
4. Rectal biopsy
Treatment
A procedure called serial rectal irrigation helps alleviate pressure in (decompress) the bowel.
The abnormal section of colon must be removed using surgery.
Most often, the rectum and abnormal part of the colon are removed.
The healthy part of the colon is then pulled down and attached to the anus.
Sometimes this can be done in 1 operation.
It is often done in 2 parts.
A colostomy is performed first.
The other part of the procedure is done later in the child's first year of life.
The most often performed repairs are the Swenson, Duhamel, and Soave procedures.
Several other creative methods have been done, such as:
1. A modified transanal method with trans-abdominal open or laparoscopic assistance,
2. Single-incision laparoscopic endorectal pull-through (SILEP), and
3. Natural orifice trans-luminal endoscopic surgery (NOTES)
Regeneration cell treatments are under studies to return function in aganglionic intestine.
TABLE OF CONTENT
Introduction
Chapter 1 Hirschsprung’s Disease
Chapter 2 Causes
Chapter 3 Symptoms
Chapter 4 Diagnosis
Chapter 5 Treatment
Chapter 6 Prognosis
Chapter 7 Intussusception
Chapter 8 Volvulus
Epilogue

• Language: English
• Publisher: Kenneth Kee
• Release date: Mar 17, 2017
• ISBN: 9781370527496

Kenneth Kee

Medical doctor since 1972.Started Kee Clinic in 1974 at 15 Holland Dr #03-102, relocated to 36 Holland Dr #01-10 in 2009.Did my M.Sc (Health Management ) in 1991 and Ph.D (Healthcare Administration) in 1993.Dr Kenneth Kee is still working as a family doctor at the age of 74However he has reduced his consultation hours to 3 hours in the morning and 2 hours inthe afternoon.He first started writing free blogs on medical disorders seen in the clinic in 2007 on http://kennethkee.blogspot.com.His purpose in writing these simple guides was for the health education of his patients which is also his dissertation for his Ph.D (Healthcare Administration). He then wrote an autobiography account of his journey as a medical student to family doctor on his other blog http://afamilydoctorstale.blogspot.comThis autobiography account “A Family Doctor’s Tale” was combined with his early “A Simple Guide to Medical Disorders” into a new Wordpress Blog “A Family Doctor’s Tale” on http://ken-med.com.From which many free articles from the blog was taken and put together into 1000 eBooks.He apologized for typos and spelling mistakes in his earlier books.He will endeavor to improve the writing in futures.Some people have complained that the simple guides are too simple.For their information they are made simple in order to educate the patients.The later books go into more details of medical disorders.He has published 1000 eBooks on various subjects on health, 1 autobiography of his medical journey, another on the autobiography of a Cancer survivor, 2 children stories and one how to study for his nephew and grand-daughter.The purpose of these simple guides is to educate patient on health disorders and not meant as textbooks.He does not do any night duty since 2000 ever since Dr Tan had his second stroke.His clinic is now relocated to the Buona Vista Community Centre.The 2 units of his original clinic are being demolished to make way for a new Shopping Mall.He is now doing some blogging and internet surfing (bulletin boards since the 1980's) startingwith the Apple computer and going to PC.The entire PC is upgraded by himself from XT to the present Pentium duo core.The present Intel i7 CPU is out of reach at the moment because the CPU is still expensive.He is also into DIY changing his own toilet cistern and other electric appliance.His hunger for knowledge has not abated and he is a lifelong learner.The children have all grown up and there are 2 grandchildren who are even more technically advanced than the grandfather where mobile phones are concerned.This book is taken from some of the many articles in his blog (now with 740 posts) A Family Doctor’s Tale.Dr Kee is the author of:"A Family Doctor's Tale""Life Lessons Learned From The Study And Practice Of Medicine""Case Notes From A Family Doctor"

Book preview

Hirschsprung’s Disease,

A

Simple

Guide

To

The Condition,

Diagnosis,

Treatment

And

Related Conditions

By

Dr Kenneth Kee

M.B.,B.S. (Singapore)

Ph.D (Healthcare Administration)

Copyright Kenneth Kee 2017 Smashwords.com

Published by Kenneth Kee at Smashwords.com

Dedication

This book is dedicated

To my wife Dorothy

And my children

Carolyn, Grace

And Kelvin

This book describes the Hirschsprung’s Disease, Diagnosis and Treatment and Related Diseases which is seen in some of my patients in my Family Clinic.

(What You Need to Treat Hirschsprung’s Disease)

This eBook is licensed for the personal enjoyment only. This eBook may not be re-sold or given away to other people. If you would like to share this book with another person, please purchase an additional copy for each reader.

If you’re reading this book and did not purchase it, or it was not purchased for your use only, then please return to Smashwords.com and purchase your own copy.

Thank you for respecting the hard work of this author.

Introduction

I have been writing medical articles for my blog http://kennethkee.blogspot.com (A Simple Guide to Medical Condition) for the benefit of my patients since 2007.

My purpose in writing these simple guides was for the health education of my patients.

Health Education was also my dissertation for my Ph.D (Healthcare Administration).

I then wrote an autobiolographical account of his journey as a medical student to family doctor on his other blog http://afamilydoctorstale.blogspot.com.

This autobiolographical account A Family Doctor’s Tale was combined with my early A Simple Guide to Medical Conditions into a new Wordpress Blog A Family Doctor’s Tale on http://kenkee481.wordpress.com.

From which many free articles from the blog was taken and put together into 700 amazon kindle books and some into Smashwords.com eBooks.

Some people have complained that the simple guides are too simple.

For their information they are made simple in order to educate the patients.

The later books go into more details of medical conditions.

The first chapter is always from my earlier blogs which unfortunately tends to have typos and spelling mistakes.

Since 2013, I have tried to improve my spelling and writing.

As I tried to bring you the latest information about a condition or illness by reading the latest journals both online and offline, I find that I am learning more and improving on my own medical knowledge in diagnosis and treatment for my patients.

Just by writing all these simple guides I find that I have learned a lot from your reviews (good or bad), criticism and advice.

I am sorry for the repetitions in these simple guides as the second chapters onwards have new information as compared to my first chapter taken from my blog.

I also find repetition definitely help me and maybe some readers to remember the facts in the books more easily.

I apologize if these repetitions are irritating to some readers.

Chapter 1

Hirschsprung’s disease

What is Hirschsprung's disease?

Hirschsprung’s disease is a congenital disorder causing blockage of the large intestine.

It happens due to poor muscle movement in the bowel.

It is a congenital disorder meaning that it is present from birth.

Physiopathology:

The